Cutaneous angiosarcoma associated with the Kasabach-Merritt syndrome.

نویسندگان

  • Sue May Tan
  • Yong Kwang Tay
  • Tsun Tsien Liu
  • Kent Mancer
چکیده

Dear Editor, Angiosarcoma is a rare tumour commonly affecting elderly men, usually occurring on the head and neck region.1 The tumour usually presents as ecchymosis-like plaques, and less commonly with haemorrhage, oedema, ulceration and recurrent facial angioedema. Kasabach-Merritt syndrome (KMS) may occur in association with a vascular tumour and is characterised by consumption of platelets and coagulation factors within the tumour.2 This syndrome has been described mostly in children; only a few cases have been associated with angiosarcoma in adults. We report a case of cutaneous angiosaroma of the scalp in an elderly man associated with KMS.

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عنوان ژورنال:
  • Annals of the Academy of Medicine, Singapore

دوره 39 12  شماره 

صفحات  -

تاریخ انتشار 2010