Cutaneous angiosarcoma associated with the Kasabach-Merritt syndrome.
نویسندگان
چکیده
Dear Editor, Angiosarcoma is a rare tumour commonly affecting elderly men, usually occurring on the head and neck region.1 The tumour usually presents as ecchymosis-like plaques, and less commonly with haemorrhage, oedema, ulceration and recurrent facial angioedema. Kasabach-Merritt syndrome (KMS) may occur in association with a vascular tumour and is characterised by consumption of platelets and coagulation factors within the tumour.2 This syndrome has been described mostly in children; only a few cases have been associated with angiosarcoma in adults. We report a case of cutaneous angiosaroma of the scalp in an elderly man associated with KMS.
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ورودعنوان ژورنال:
- Annals of the Academy of Medicine, Singapore
دوره 39 12 شماره
صفحات -
تاریخ انتشار 2010